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Astrocyte Myotonic dystrophy mouse models Astrocytes Brain Intermediate filament CTG repeat contractions Gene editing Acetylcholinesterase deficiency Acute coronary syndrome Central nervous system Brain dysfunction Maximal force MBNL ACETYLCHOLINESTERASE Aging RNA splicing Mouse models DM1 Hypoxia Dystrophie Myotonique Transcriptomics Skeletal muscle CRISPR/Cas9 RNA biology Myotonic Dystrophy Transgenic mouse Centronuclear myopathy Dystrophin CMS CONGENITAL MYATHENIC SYNDROME Antisense oligonucleotides Trinucleotide repeat expansion Cardiac muscle Gene therapy KNOCKOUT MICE Myotonic Dystrophy Type 1 Myotonic dystrophy CRISPRi Gene Therapy Cell penetrating peptide Expression CTG repeat instability Myotonic dystrophy type 1 GABA Glutamate CTG repeats Therapy Long read sequencing Exercise Neuron Autophagy GSK3␤ Diaphragm Muscle Cytoskeleton Myotonic Dystrophy type 1 Acetylcholinesterase knockout mouse Oligodendrocytes Cell culture model Dynamin 2 Lc3 Glucocorticoid-receptor Humans Desmin Muscular dystrophy Dystrophie myotonique Myelin Dilated cardiomyopathy RNA interference Mouse model DMSXL mice Glucocorticoids Heart In vivo Antisense oligonucleotide Trinucleotide Repeat Expansion PacBio Animals Mice Thérapie génique Transgenic mouse model DMPK ARN Glial cells Cell model Heart failure Knockout BIOLOGIE MOLECULAIRE Fibrosis PCR AAV Alternative splicing Quantitative microdialysis Oligodendrocyte Genotype phenotype correlation Male Exercice Motoneuron Myostatin Duchenne muscular dystrophy